tests
- Glutaryl-CoA dehydrogenase
- 3-Hydroxy-isobutyryl-CoA hydrolase (HIBCH)
- 3-Hydroxy-isobutyric acid dehydrogenase (HIBADH)
- Propionyl-CoA carboxylase (PCC)
- Short branched-chain acyl-CoA dehydrogenase (SBCAD)
- 2-methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD)
- Isovaleryl-CoA dehydrogenase (IVD)
- 3-Methyl-crotonyl-CoA carboxylase (MCC)
- 3-Methyl-glutaconyl-CoA hydratase (MGH)