Laboratory Genetic Metabolic Diseases AMC

description / indication

Barth syndrome. Screening test in dried bloodspot, confirmation in lymphocytes, fibroblasts or tissue

MethodLC tandem MS
Test frequency2 weeks (excl. culture time for fibroblasts)
Price€ 140

materials

materialblood
amount5 ml
conditionsroom temperature
specificsBlood samples need to arrive in our laboratory within 48 hours after drawing.
materialbloodspot
amount1 dried bloodspot, 40 µl of blood on a guthrie card
conditionsroom temperature
materialCultured fibroblasts
conditionsDo not freeze or heat the samples!
specificsGrow the cells to near confluence in a T-25 flask, fill the flask completely with sterile culture media, cap the flasks tightly and wrap the cap with parafilm. Label the flask clearly with identifying information and date of collection, wrap in protective material and place in a sealed plastic bag in the Styrofoam shipping box.
materiallymphocytes
conditionsdry ice
specificsIsolated lymphocytes from EDTA/Heparin blood sample of patient and 1 control should be sent in clearly labeled, tightly capped tubes (incl. patient info), stored at minus 80 degrees Celsius (-80 ºC) and subsequently shipped on dry ice to lab GMD.
materialtissue
conditions
specificsContact metabolite diagnostics first